Mucopolysaccharidosis Type VI also known as Maroteaux-Lamy syndrome is an error of mucopolysaccharide metabolism characterized by excretion of dermatan sulfate in the urine, growth retardation, lumbar kyphosis, sternal protrusion, genu valgum, usually hepatosplenomegaly, and no mental retardation; onset occurs after 2 years of age.
Drugs used to treat Mucopolysaccharidosis Type VI
Name | Drug Class |
---|---|
Galsulfase | Lysosomal enzymes |
Naglazyme | Lysosomal enzymes |